Juvenile Rheumatoid Arthritis – Part Two
The oligoarticular type of juvenile arthritis, which has fewer joints affected, is indicated by four or fewer joints being inflamed with the ankles and knees, the larger joints, being more commonly affected. The children present as feeling well but may exhibit a limp when they walk. If the child appears to only have one hip affected then the diagnosis should be questioned as they are more likely to have a different condition such as Perthes disease. Chronic arthritic problems can lead to weakness and wasting of the main extensor muscles of the knee, with tightness of the hamstrings leading to a flexion contracture of the knee. Asymmetric arthritis just in one leg can produce a leg length discrepancy.
The many joint affected type of disease (polyarticular) is characterised by having at least five joints affected, typically in a symmetrical pattern with the same joints affected on both sides. The child may have a low grade fever and if there are significant limits of joint movement this is associated with weakness of the relevant muscles and decreased normal function. A thorough physical examination of the child is very important for the correct diagnosis of juvenile arthritis as this will indicate where the problems lie and which kind of juvenile arthritis the patient has.
Settling on the diagnosis of juvenile arthritis depends on a joint showing an effusion which is the presence of inflammatory fluid within the joint, along with other symptoms and signs such as warmth, redness, limited range of motion and pain. Some joints may have an effusion which is not apparent such as the hip, but they can still show limited movement of the joint and pain. It may not be possible to establish the diagnosis of juvenile arthritis as the fever and rashes may come on initially without the arthritis at the time, with the arthritis appearing later by several months. Enlargement of lymph nodes and the liver and tenderness of muscles may be evident.
In the polyarticular form of arthritis where many joints are inflamed, it is common for there to be a symmetrical involvement of the weight bearing joints as well as smaller ones of the hand. The joint cartilage may be reduced in thickness with eroded areas and in some joints the formation of a fusion across them. With more chronic changes there can be thickened synovial membranes and joint effusions, subluxations (partial dislocations), joint contractures and stiffness, bony deformity (particularly the fingers) and bony enlargements. The joints can also lose bone mass and suffer narrowing of the joint spaces as the cartilage thins.
A reduction of extension in the neck may not produce any symptoms but it is important to identify this as it can indicate arthritic changes in the cervical spine which can lead to partial dislocation (subluxation) of the upper neck bones, a potentially dangerous situation. The neck bones can also fuse together along the posterior structures. The jaw joints, the tempero-mandibular joints, may also be affected and lead to reduced amount of growth in the lower jaw with inability to open the mouth as wide as normal. There may also be involvement of the eyes in the inflammatory process.
Juvenile arthritis and other complex conditions are best managed by a specialised multidisciplinary team due to the numerous problems which patients have to do with family and patient education and schooling, drug treatments, physiotherapy and occupational therapy. It is rarely if ever successful to give isolated treatments to this patient group. Reviewing patients at regular intervals allows the drug treatments to be fine tuned towards a reduction in the morning stiffness and towards fewer affected joints until no symptomatic joints remain. A typical team to manage these conditions may include a physiotherapist, occupational therapist, social workers, a paediatric rheumatologist and nurse.
Surgery is not routinely indicated for most of these patients although joint injections with steroids may be employed for some. Polyarticular arthritis patients may suffer severe knee and hip arthritis which can be treated with knee and hip replacement once skeletal maturity has been reached and bone growth has stopped. Encouraging patients to be active is important as resting for long periods is not helpful and more active patients do better.
Jonathan Blood Smyth is the Superintendent of Physiotherapy at an NHS hospital in the South-West of the UK. He writes articles about back pain, neck pain, and injury management. If you are looking for Physiotherapist Croydon visit his website.